Pseudoxanthoma elasticum (PXE) is an inherited disorder characterized by generalized fragmentation and progressive calcification of elastic tissue.We report two sporadic cases of PXE, both of whom presented here with asymptomatic yellowish papules over the flexural sites for cosmetic reasons.Histopathological findings on hematoxylin and eosin and Verhoeff-Van Gieson (VVG) staining were classical of PXE.In addition to this, renal calcification was documented on plain radiography of kidneys, ureters, and bladder (KUB) in both the cases.
Paucity of literature describing ice blue graphic tee the association of nephrocalcinosis with PXE prompted the present report.